Category:Phenylalanine-4-hydroxylase

Abbrev	PAH +
CurationStatus	uncurated +
DefiningCitation	Kaufman, D (1 February 1958). "A New Cofactor Required for the Enzymatic Conversion of Phenylalanine to Tyrosine.". J. Biol. Chem. 230 (230): 931–39. +
Definition	Phenylalanine hydroxylase (EC 1.14.16.1) i … Phenylalanine hydroxylase (EC 1.14.16.1) is an enzyme which catalyses the reaction responsible for the addition of a hydroxyl group to the end of the 6-carbon aromatic ring of phenylalanine, such that it becomes tyrosine. Phenylalanine hydroxylase is the rate-limiting enzyme of the metabolic pathway which degrades excess phenylalanine. The PAH gene or a 1:1 ortholog thereof encodes for phenylalanine hydroxylase. eof encodes for phenylalanine hydroxylase.
Has role	Enzyme +
Id	PRO:000012234 +
Is part of	Catecholamine system +, Adrenergic system +, Dopaminergic system +, Noradrenergic system +
Label	Phenylalanine-4-hydroxylase +
Modification dateThis property is a special property in this wiki.	1 May 2010 05:10:04 +
ModifiedDate	1 May 2010 +
PMID	13525410 +
RelatedTo	L-Tyrosine +, L-Phenylalanine +
SuperCategory	Protein +
Synonym	Phe-4-monooxygenase +, Phenylalanine hydroxylase +
Categories	Protein

Epinephrine +, L-Phenylalanine +, Levodopa +, Norepinephrine +, Tetrahydrobiopterin +	RelatedTo

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